Is Auditory Neuropathy an Appropriate Diagnosis if There Is No Neuropathy

作者: Roger R. Marsh , Ken Kazahaya

DOI: 10.1007/978-4-431-09433-3_16

关键词:

摘要: In the initial reports of auditory neuropathy, there was ample evidence that patients did indeed have neuropathy—a disease or disorder nerve other peripheral nerves. years followed, diagnosis has been applied to all cases in which cochlear microphonic potentials otoacoustic emissions were present and brainstem response absent, whether not known be affected. At one time an argument could made lesion presumed because it proven selective inner hair cell impairment even existed as a clinical entity. It become clear, however, mutations OTOF gene, perhaps genes, can cause defect function is quite different from true neuropathy. These differ those with neuropathy age onset, severity loss, prognosis, often potential for benefit implantation. The come reserve nerve.

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