Sudden unexpected death in children with a previously diagnosed cardiovascular disorder.

摘要: Background: It is known that children with previously diagnosed heart defects die suddenly. The causes of death are often unknown. Objective: aim the study was to identify all infants and within Netherlands disease who had a sudden unexpected (SUD), possible cause death. Design: Retrospective, cross-sectional study. Patients setting: All (<19 years) defect SUD between January 1990 June 2001 in seven out eight tertiary centres were identified using hospital databases. We excluded patients receiving compassionate care. Diagnoses, clinical status circumstances sought from case notes post mortem reports. Deaths classified as cardiac or non-cardiac origin. Results: 150 cases (89 male) at median age 2.3 years (range 18 days–18.9 years); 49/150 (33%) ≤1 year. Diagnostic categories included left right shunts (N=34, 14 year), cyanotic lesions (N=38, 13 yar), cardiomyopathy (N=11, 2 univentricular (N=24, 10 obstructive 3 arrhythmia (N=8, 0 miscellaneous (N=18, 5 year). 108/150 (72%) been operated whom 61 (57%) corrective surgery. Of SUD, 32/49 (65%) undergone surgery (11 corrective); 76/101 older previous (50 corrective). 114/150 (76%) died cause. Causes arryhythmia (59), failure (25), shunt occlusion (10), pulmonary hypertensive crisis (8) acute myocardial infarction (4). 30/49 (61%) cause; arrythmia (8), (7), (2). Conclusions: predominantly Pumpfailure arrhythmias terminal events significant number entire population.