Mortality ratios, life expectancy, and causes of death in patients with Turner's syndrome.

作者: W H Price , J F Clayton , S Collyer , R De Mey , J Wilson

DOI: 10.1136/JECH.40.2.97

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摘要: In a prospective study of 156 female patients with Turner's syndrome who had survived infancy and been followed up for an average 17 years there were 15 deaths. The expected mortality was 3.6. Sixteen the congenital heart anomaly five deaths occurred in this group. 10 remaining 140 three times as many expected. reduction life expectation 12.5 at age 1 year, 11 20, 40. Deaths due to broad spectrum diseases. sample whole eight from diseases circulatory system. This number is significantly greater than expected, but four disease. When disease omitted disorders not increased. Within category dissection aorta, which greatly excess Two these no previous evidence

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