Prédisposition génétique et infections de l'enfant

作者: C. Picard , O. Filipe-Santos , A. Chapgier , H. von Bernuth , G. Vogt

DOI: 10.1016/J.ARCPED.2006.07.009

关键词:

摘要: The classic primary immunodeficiencies confer predisposition to multiple infectious diseases. However since ten years severe pediatric infections which were idiopathic have now molecular explanation. Indeed, defects in several genes a infection with specific pathogenes otherwise healthy individuals. These children present new kind of hereditary immunodeficiency and/or recurrent caused by only one microorganisms family, opposition others patients "classic" immunodeficiency.

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