摘要: Hereditary neutropenia includes many disorders of distinct origin and variable prognosis, characterized by a reduction the absolute neutrophil count (ANC) that predisposes patients to bacterial infections, in particular pyogenic such as cutaneous cellulitis, deep abscesses, pneumonia sepsis [1, 2]. Susceptibility even with severe neutropenia, can be quite variable, depending on underlying etiology. Congenital my associated extraematopoietic manifestations.
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