Bardet-Biedl Syndrome proteins regulate intracellular signaling and neuronal function in patient-specific iPSC-derived neurons
Rudolph L. Leibel , Sharon Wardlaw , Charles A. Leduc , Lisa C. Burnett
Journal of Clinical Investigation 131 ( 8) 146287
1
2021
Altered function and maturation of primary cortical neurons from a 22q11.2 deletion mouse model of schizophrenia.
Ziyi Sun , Damian J. Williams , Bin Xu , Joseph A. Gogos
Translational Psychiatry 8 ( 1) 85
12
2018
Rapid modification of proteins using a rapamycin-inducible tobacco etch virus protease system.
Damian J. Williams , Henry L. Puhl , Stephen R. Ikeda
PLOS ONE 4 ( 10)
40
2009
Differentiation of hypothalamic-like neurons from human pluripotent stem cells
Liheng Wang , Kana Meece , Damian J. Williams , Kinyui Alice Lo
Journal of Clinical Investigation 125 ( 2) 796 -808
74
2015
Inhibition of N-type calcium channels by activation of GPR35, an orphan receptor, heterologously expressed in rat sympathetic neurons.
Juan Guo , Damian J. Williams , Henry L. Puhl , Stephen R. Ikeda
Journal of Pharmacology and Experimental Therapeutics 324 ( 1) 342 -351
50
2008
Rbfox Splicing Factors Promote Neuronal Maturation and Axon Initial Segment Assembly.
Martin Jacko , Sebastien M. Weyn-Vanhentenryck , John W. Smerdon , Rui Yan
Neuron 97 ( 4) 853 -8686
43
2018
Mechanisms involved in nicotinic acetylcholine receptor-induced neurotransmitter release from sympathetic nerve terminals in the mouse vas deferens.
Damian J. Williams , Peter Sidaway , Thomas C. Cunnane , Keith L. Brain
PLOS ONE 6 ( 12)
5
2011
Intranuclear Microinjection of DNA into Dissociated Adult Mammalian Neurons
Van B. Lu , Damian J. Williams , Yu-Jin Won , Stephen R. Ikeda
Journal of Visualized Experiments ( 34)
17
2009
Bioreactor model of neuromuscular junction with electrical stimulation for pharmacological potency testing
Surapon N. Charoensook , Damian J. Williams , Syandan Chakraborty , Kam W. Leong
Integrative Biology 9 ( 12) 956 -967
9
2017
N-arachidonoyl L-serine, a putative endocannabinoid, alters the activation of N-type Ca2+ channels in sympathetic neurons.
Juan Guo , Damian J. Williams , Stephen R. Ikeda
Journal of Neurophysiology 100 ( 2) 1147 -1151
24
2008
A Stem Cell-Based Screening Platform Identifies Compounds that Desensitize Motor Neurons to Endoplasmic Reticulum Stress.
Sebastian Thams , Emily Rhodes Lowry , Marie-Hélène Larraufie , Krista J. Spiller
Molecular Therapy 27 ( 1) 87 -101
11
2019
Modulation of neurite outgrowth by activation of calcium-permeable kainate receptors expressed by rat nociceptive-like dorsal root ganglion neurons.
Donald J. Joseph , Damian J. Williams , Amy B. MacDermott
Developmental Neurobiology 71 ( 10) 818 -835
19
2011
Synergistic binding of transcription factors to cell-specific enhancers programs motor neuron identity
Hynek Wichterle , Esteban O Mazzoni , Esteban O Mazzoni , Shaun Mahony
PMC
208
2013
Human stem cell model of HNF1A deficiency shows uncoupled insulin to C-peptide secretion with accumulation of abnormal insulin granules
Rudolph L Leibel , Jesper Gromada , Jose Oberholzer , Charles A LeDuc
bioRxiv
8
2021
A functionally characterized test set of human induced pluripotent stem cells
Gabriella L *Boulting , Evangelos *Kiskinis , Gist F *Croft , Mackenzie W *Amoroso
Nature Biotechnology 29 ( 3) 279 -286
412
2011
A Simple, Highly Efficient Method for Heterologous Expression in Mammalian Primary Neurons Using Cationic Lipid-mediated mRNA Transfection
Damian J Williams , Henry L Puhl III , Stephen R Ikeda ,
Frontiers in Neuroscience 4 181 -181
67
2010
The sources and sequestration of Ca2+ contributing to neuroeffector Ca2+ transients in the mouse vas deferens
Keith L Brain , Alina M Cuprian , Damian J Williams , Thomas C Cunnane
The Journal of physiology 553 ( 2) 627 -635
32
2003
Reduced calcium levels and accumulation of abnormal insulin granules in stem cell models of HNF1A deficiency
Bryan J González , Haoquan Zhao , Jacqueline Niu , Damian J Williams
Communications Biology 5 ( 1) 779 -779
15
2022
Epilepsy in a mouse model of GNB1 encephalopathy arises from altered potassium (GIRK) channel signaling and is alleviated by a GIRK inhibitor
Sophie Colombo , Haritha P Reddy , Sabrina Petri , Damian J Williams
Frontiers in Cellular Neuroscience 17 1175895 -1175895
3
2023
Behavioral control through the direct, focal silencing of neuronal activity
Anna V Elleman , Nikola Milicic , Damian J Williams , Jane Simko
Cell Chemical Biology
2024