Malformations of the craniocervical junction (chiari type I and syringomyelia: classification, diagnosis and treatment)

摘要: Chiari disease (or malformation) is in general a congenital condition characterized by an anatomic defect of the base skull, which cerebellum and brain stem herniate through foramen magnum into cervical spinal canal. The onset syndrome symptoms usually occurs second or third decade (age 25 to 45 years). Symptoms may vary between periods exacerbation remission. diagnosis type I malformation patients with without established neuroimaging techniques. most effective therapy for malformation/syringomyelia surgical decompression magnum, however there are non-surgical relieve neurophatic pain: either pharmacological non-pharmacological. Pharmacological use drugs that act on different components pain. Non-pharmacological therapies primarly based peripheral electrical stimulation. It important determine needs terms health-care, social, educational, occupational, relationship issues, addition those derived from information aspects, particularly at symptoms. Currently, no consensus among specialists regarding etiology how approach, monitor, follow-up, treat condition. necessary physicians involved care people this comprehensively approach management follow-up patients, they organize interdisciplinary teams including all professionals can help increase quality life patients.