Paraneoplastic autoimmune multiorgan syndrome (paraneoplastic pemphigus) with unusual manifestations and without detectable autoantibodies.
作者： Jimena Sanz-Bueno , Daniella Cullen , Carlos Zarco , Francisco Vanaclocha
关键词: Lichenoid eruption 、 Paraneoplastic pemphigus 、 Autoimmune hepatitis 、 Pathology 、 Medicine 、 Pathogenesis 、 Autoantibody 、 Vitiligo 、 Immunology 、 Bronchiolitis obliterans 、 Leukemia
摘要: We describe a patient with paraneoplastic autoimmune multiorgan syndrome (PAMS) secondary to lymphoblastic T- cell lymphoma who presented lichenoid dermatitis and vitiligo, later developing bronchiolitis obliterans hepatitis. Notably, he had no detectable autoantibodies. The development of vitiligo hepatic involvement probably indicate role for cytotoxic lymphocytes in the pathogenesis this syndrome.
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Grant J. Anhalt, SooChan Kim, John R. Stanley, Neil J. Korman, Douglas A. Jabs, Mark Kory, Hiroshi Izumi, Harry Ratrie, Diya Mutasim, Lina Ariss-Abdo, Ramzy S. Labib, Paraneoplastic Pemphigus New England Journal of Medicine. ,vol. 323, pp. 1729- 1735 ,(1990) , 10.1056/NEJM199012203232503