Congenital short QT syndrome.

摘要: Long QT intervals in the ECG have long been associated with sudden cardiac death. The congenital syndrome was first described individuals structurally normal hearts 1957.1 Little known about significance of a short interval. In 1993, after analyzing 6693 consecutive Holter recordings Algra et al concluded that an increased risk death present not only patients interval, but also interval (<400 ms).2 Because this retrospective analysis, further evaluation data possible. It until 2000 short-QT (SQTS) proposed as new inherited clinical by Gussak al.3 initial report two siblings and their mother all whom displayed persistently youngest 17 year old female presenting several episodes paroxysmal atrial fibrillation requiring electrical cardioversion.3 Her measured 280 msec at heart rate 69. 21 brother 272 58, whereas 51 showed 260 74. authors noted similar findings another unrelated 37 patient