Pseudo-pseudomyxoma peritonei from peritoneal sarcomatosis

摘要: Background: Pseudomyxoma peritonei (PMP) is a rare clinical entity of mucinous ascites, most commonly associated with appendiceal neoplasms. Cytoreductive surgery (CRS) and hyperthermic intraperitoneal chemotherapy (HIPEC) remains the current standard care for PMP. Peritoneal sarcomatosis (PS) an exceptionally disease poor prognosis. PMP PS has not been previously described. The role cytoreductive or without well-defined. manifesting like Case presentation: A 74-year-old patient several weeks history vague abdominal pain increased girth was referred to our facility after incidental finding during laparoscopic inguinal hernia repair. After complete work-up, he advised undergo CRS/HIPEC. Intra-operatively, noted have extensive ascites underwent aggressive CRS HIPEC Result: Final pathology revealed myxoid liposarcoma mucin dissemination, which confirmed cytogenetic analysis. Conclusion: We describe case pseudomyxoma originating from intra-abdominal sarcoma. propose term “pseudo-pseudomyxoma peritonei” appropriately this unusual event.