Pseudomyxoma peritonei – a revisit: report of 2 cases and literature review

作者: Chunyanca Li , Rani Kanthan , SC Kanthan

DOI: 10.1186/1477-7819-4-60

关键词: DiseaseMedicineAppendixDebridementGeneral surgeryPseudomyxoma peritoneiClinical courseMucinous AscitesChemotherapySurgical oncology

摘要: Pseudomyxoma peritonei (PMP) is a rare, chronic, relapsing, diagnostically challenging and poorly understood disease characterized by disseminated mucinous ascites peritoneal implants. We report two cases of PMP that represent the biological variants d isseminated p eritoneal denom ucinosis (DPAM) – benign variant m ucinous c arcinoma tosis (PMCA) malignant variant, both which were multiple relapses progression despite aggressive management. Even with better understanding recent advances in management these cases, remains an enigmatic protracted clinical course recurrences surgery and/or chemotherapy. Recognition as delayed consequence years later should alert all surgeons to be extremely vigilant when treating neoplasms appendix, special care being directed towards adequate excision thorough debridement at initial diagnosis.

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