Impaired Elastogenesis in Hurler Disease: Dermatan Sulfate Accumulation Linked to Deficiency in Elastin-Binding Protein and Elastic Fiber Assembly
作者： Aleksander Hinek , Sarah E. Wilson
DOI: 10.1016/S0002-9440(10)64961-9
关键词: Hurler syndrome 、 Biochemistry 、 Biology 、 Elastic fiber assembly 、 Chondroitin sulfate B 、 Cell biology 、 Dermatan sulfate 、 Elastic fiber 、 Elastin 、 Tropoelastin 、 Heparan sulfate
摘要: … Because cultured Hurler fibroblasts proliferate more quickly than their normal counterparts and the addition of exogenous insoluble elastin reduces their proliferation, we suggest that …
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