Nephrotic syndrome in 1st year of life and the role of unilateral nephrectomy.
作者： Tej K. Mattoo , Abdul M. Al-Sowailem , Mansoor S. Al-Harbi , Mustapha A. Mahmood , Yousef Katawee
DOI: 10.1007/BF00856821
关键词: Renal biopsy 、 Congenital nephrotic syndrome 、 Glomerulopathy 、 Surgery 、 Bilateral Nephrectomy 、 Nephrectomy 、 Focal segmental glomerulosclerosis 、 Nephrotic syndrome 、 Glomerulonephritis 、 Medicine
摘要: The study includes 17 infants with nephrotic syndrome. Their ages at the onset of disease ranged from 10 days to months (median 2 months), and included males 7 females. Ten patients had consanguineous parents 4 a history similar illness in sibling. Renal biopsy revealed diffuse mesangial proliferation patients, sclerosis 3, Finnish microcystic 2, focal segmental glomerulosclerosis atypical glomerulopathy 1 each. Unilateral nephrectomy was performed 8 intractable proteinuria associated multiple complications. Five are well after 4–36 follow-up, died septicaemia soon procedure, needed dialysis is stable 26 showed no reduction degree proteinuria. We conclude that unilateral better alternative bilateral some severe
springer.com
sci-hub.se 参考文章(11)
David S. Celermajer, Reuben Baumal, Paul S. Thorner, Gerald S. Arbus, Focal segmental glomerulosclerosis and progressive renal failure associated with a unilateral kidney. Pediatrics. ,vol. 73, pp. 806- 810 ,(1984)
B.S. Kaplan, M.A. Bureau, K.N. Drummond, The nephrotic syndrome in the first year of life: is a pathologic classification possible? The Journal of Pediatrics. ,vol. 85, pp. 615- 621 ,(1974) , 10.1016/S0022-3476(74)80502-0
Malcolm G. Coulthard, Management of Finnish congenital nephrotic syndrome by unilateral nephrectomy Pediatric Nephrology. ,vol. 3, pp. 451- 453 ,(1989) , 10.1007/BF00850226
Y. Oka, K. Fujiwara, H. Endou, Epidermal growth factor in the mouse kidney: developmental changes and intranephron localizations. Pediatric Nephrology. ,vol. 2, pp. 124- 128 ,(1988) , 10.1007/BF00870392
John D. Mahan, S. Michael Mauer, Richard K. Sibley, Robert L. Vernier, Congenital nephrotic syndrome: Evolution of medical management and results of renal transplantation The Journal of Pediatrics. ,vol. 105, pp. 549- 557 ,(1984) , 10.1016/S0022-3476(84)80418-7
Tej K Mattoo, A Baez Giangreco, Mohammad Afzal, Mohammad Akhtar, None, Cystic lymphangiectasia of the kidneys in an infant with nephrotic syndrome Pediatric Nephrology. ,vol. 4, pp. 228- 232 ,(1990) , 10.1007/BF00857660
Tej K Mattoo, Mohammad Akhtar, None, Familial glomerulopathy with proximal tubular dysfunction: a new syndrome? Pediatric Nephrology. ,vol. 4, pp. 223- 227 ,(1990) , 10.1007/BF00857659
Tej K. Mattoo, Mustapha A. Mahmood, Mansoor S. Al-Harbi, Nephrotic syndrome in Saudi children clinicopathological study of 150 cases Pediatric Nephrology. ,vol. 4, pp. 517- 519 ,(1990) , 10.1007/BF00869837
Richard K. Sibley, John Mahan, S. Michael Mauer, Robert L. Vernier, A clinicopathologic study of forty-eight infants with nephrotic syndrome Kidney International. ,vol. 27, pp. 544- 552 ,(1985) , 10.1038/KI.1985.45
Massimo Chiossi F, Castellani R, Crisalli M, Congenital nephrotic syndrome La Pediatria. ,vol. 77, pp. 304- 317 ,(1969)