Unusual causes of extrahepatic biliary obstruction in children: a case series with review of literature

摘要: This paper highlights the etiology, diagnosis, management and outcome in nine unusual cases of extrahepatic biliary obstruction children. Extrahepatic atresia choledochal cyst constituted 127 out 136 (93%) all pediatric surgical disorders managed between March 2000 February 2007 at reporting centre. However, children (aged 1.5–15 years) presented with uncommon causes like (1) idiopathic benign non-traumatic inflammatory stricture (n = 3), (2) fibrosing chronic pancreatitis 2), (3) post-cholecystectomy type 4 1), (4) post-acute pseudo-cyst pancreas (5) non-Hodgkin's lymphoma (NHL) extramural common bile duct compression gall bladder perforation (6) Langerhan cell histiocytosis (LCH, n 1). The clinical features diagnostic work up each group are discussed. A preoperative endoscopic/percutaneous drainage was required four because cholangitis presentation. biliary-enteric anastomosis performed for seven groups (1)–(4). patients NHL LCH were referred chemotherapy after establishing tissue diagnosis laparotomy. With a follow-up period 3 months to 7 years, (with exception LCH) currently anicteric. draws attention some infrequently discussed entails carefully planned combination endoscopic interventions, interventional radiology surgery. is usually satisfactory.