Presentation of a child with Ehlers-Danlos syndrome type- IV with acute abdomen a case report

作者: Hüseyin Murat Mutus , Çiğdem Ulukaya Durakbasa , Mevlit Korkmaz , Selma Fettahoğlu , Aytekin Kaymakcı

DOI:

关键词: SurgeryEhlers-Danlos syndrome type IVHeterogeneous groupRuptured abdominal aortic aneurysmPresentation (obstetrics)Connective tissueMedicineAcute abdomen

摘要: Ehlers-Danlos Syndrome (EDS) is an inherited heterogeneous group of connective tissue disorders. We report a patient with EDS unknown subtype admitted to emergency room acute abdominal findings. Further investigation revealed that she had ruptured aortic aneurysm. In conclusion, probable vascular complications should be considered when presents

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