摘要: Ehlers-Danlos type VIII is a rare disorder characterized by soft, hyperextensible skin, abnormal scarring, easy bruising, and generalized periodontitis with early loss of teeth. To illustrate the clinical dermatological dental features, we present case history 20-year-old patient who has suffered from poor healing wounds at shins knees since childhood, which have developed into hyperpigmented atrophic scars. In course orthodontic treatment during last 3 years, severe apical root resorption, gingival recession, alveolar bone were observed. Family was noncontributory for any skin or tooth disorders. The typical signs confirmed diagnosis syndrome VIII. As there no specific disorder, management limited to symptomatic disease. It seems advisable consider carefully indications in patients syndrome.
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