Natural History of Portal Cavernoma Cholangiopathy

摘要: The natural history of portal cavernoma cholangiopathy (PCC) is poorly defined and understood. It develops early after acute vein thrombosis (PVT) if there failure recanalization. In PCC, the likelihood progression biliary abnormalities 1 year extremely low. PCC conveniently divided into asymptomatic symptomatic stages. majority patients with are detected incidentally on imaging. Limited data suggest that static or only slowly progressive in initial However, most workers agree that, overall, a disease. Symptomatic represents late stage its history. Finding strictures dilatation at cholangiography associated higher risk developing symptoms PCC. Onset often precipitated by development sludge calculi treating usually relieves for prolonged periods time. Clinical presentations include pain, obstructive jaundice, cholangitis, cholecystitis, other gallstone Progressive liver dysfunction secondary cirrhosis can develop minority patients.