vWF-cleaving protease/ADAMTS13

R. Martijn van der Plas, Marion E. Schiphorst, Eric G. Huizinga, Ronald J. Hené, Leo F. Verdonck, Jan J. Sixma, Rob Fijnheer, von Willebrand factor proteolysis is deficient in classic, but not in bone marrow transplantation-associated, thrombotic thrombocytopenic purpura. Blood. ,vol. 93, pp. 3798- 3802 ,(1999) , 10.1182/BLOOD.V93.11.3798

HM Tsai, Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion Blood. ,vol. 87, pp. 4235- 4244 ,(1996) , 10.1182/BLOOD.V87.10.4235.BLOODJOURNAL87104235

Miha Furlan, Rodolfo Robles, Max Solenthaler, Max Wassmer, Pierre Sandoz, Bernhard Lämmle, Deficient Activity of von Willebrand Factor–Cleaving Protease in Chronic Relapsing Thrombotic Thrombocytopenic Purpura Blood. ,vol. 89, pp. 3097- 3103 ,(1997) , 10.1182/BLOOD.V89.9.3097

M Furlan, R Robles, B Lamie, Partial purification and characterization of a protease from human plasma cleaving von Willebrand factor to fragments produced by in vivo proteolysis Blood. ,vol. 87, pp. 4223- 4234 ,(1996) , 10.1182/BLOOD.V87.10.4223.BLOODJOURNAL87104223

Taei Matsui, Taketo Shimoyama, Masanori Matsumoto, Yoshihiro Fujimura, Yoshinobu Takemoto, Masahiro Sako, Jiharu Hamako, Koiti Titani, ABO Blood Group Antigens on Human Plasma von Willebrand Factor After ABO-Mismatched Bone Marrow Transplantation Blood. ,vol. 94, pp. 2895- 2900 ,(1999) , 10.1182/BLOOD.V94.8.2895.420A03_2895_2900

ZM Ruggeri, PM Mannucci, R Lombardi, AB Federici, TS Zimmerman, Multimeric Composition of Factor VIII/von Willebrand Factor Following Administration of DDAVP: Implications for Pathophysiology and Therapy of von Willebrand's Disease Subtypes Blood. ,vol. 59, pp. 1272- 1278 ,(1982) , 10.1182/BLOOD.V59.6.1272.1272

Zaverio Ruggeri, Structure and function of von Willebrand factor. Thrombosis and Haemostasis. ,vol. 82, pp. 576- 584 ,(1992) , 10.1055/S-0037-1615883

Zaverio M. Ruggeri, Jerry Ware, von Willebrand factor. The FASEB Journal. ,vol. 7, pp. 308- 316 ,(1993) , 10.1096/FASEBJ.7.2.8440408

M. Furlan, Von Willebrand factor: molecular size and functional activity Annals of Hematology. ,vol. 72, pp. 341- 348 ,(1996) , 10.1007/S002770050184

Jefferson D. Upshaw, Congenital Deficiency of a Factor in Normal Plasma That Reverses Microangiopathic Hemolysis and Thrombocytopenia New England Journal of Medicine. ,vol. 298, pp. 1350- 1352 ,(1978) , 10.1056/NEJM197806152982407