Defective phagocytosis due to deficiencies involving the tetrapeptide tuftsin

作者: Victor A. Najjar

DOI: 10.1016/S0022-3476(75)80125-9

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摘要: A description of the symptoms and causes tuftsin deficiency is presented. Two major which give rise to a tetrapeptide (thr-lys-pro-arg) are discussed. One familial syndrome that results from an inherited mutation involving tetrapeptide. All patients history repeated infection with variable severity. parent, father or mother, deficient occasionally other siblings may have disease. The type result loss splenic function whether it due surgical removal spleen infarction infiltration organ. method for assay activity described.

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