Pulmonary vascular manifestations of hereditary hemorrhagic telangiectasia (rendu-osler disease).

作者: Vincent Cottin , Sophie Dupuis-Girod , Gaetan Lesca , Jean-François Cordier

DOI: 10.1159/000103205

关键词:

摘要: Hereditary hemorrhagic telangiectasia (HHT) or Rendu-Osler-Weber disease is a genetic disorder with autosomal dominance and variable penetrance, characterized by epistaxis, visceral

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