Quantitative Assessment of Whole-Body Tumor Burden in Adult Patients with Neurofibromatosis

作者: Scott R. Plotkin , Miriam A. Bredella , Wenli Cai , Ara Kassarjian , Gordon J. Harris

DOI: 10.1371/JOURNAL.PONE.0035711

关键词:

摘要: Purpose Patients with neurofibromatosis 1 (NF1), NF2, and schwannomatosis are at risk for multiple nerve sheath tumors premature mortality. Traditional magnetic resonance imaging (MRI) has limited ability to assess disease burden accurately. The aim of this study was establish an international cohort patients quantified whole-body internal tumor correlate clinical features disease.

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