Peripheral and cerebral metabolic features in an animal model of huntington's disease expressing full-length mutant huntingtin
作者： Carla Maria Nunes Lopes
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M. Taketo, A. C. Schroeder, L. E. Mobraaten, K. B. Gunning, G. Hanten, R. R. Fox, T. H. Roderick, C. L. Stewart, F. Lilly, C. T. Hansen, FVB/N: an inbred mouse strain preferable for transgenic analyses. Proceedings of the National Academy of Sciences of the United States of America. ,vol. 88, pp. 2065- 2069 ,(1991) , 10.1073/PNAS.88.6.2065
Pascal Kahlem, Howard Green, Philippe Djian, Transglutaminase Action Imitates Huntington's Disease: Selective Polymerization of Huntingtin Containing Expanded Polyglutamine Molecular Cell. ,vol. 1, pp. 595- 601 ,(1998) , 10.1016/S1097-2765(00)80059-3
Ulrike G A Sattler, Stefan Walenta, Wolfgang Mueller-Klieser, A bioluminescence technique for quantitative and structure-associated imaging of pyruvate. Laboratory Investigation. ,vol. 87, pp. 84- 92 ,(2007) , 10.1038/LABINVEST.3700493
T.-S. Tang, E. Slow, V. Lupu, I. G. Stavrovskaya, M. Sugimori, R. Llinas, B. S. Kristal, M. R. Hayden, I. Bezprozvanny, Disturbed Ca2+ signaling and apoptosis of medium spiny neurons in Huntington's disease. Proceedings of the National Academy of Sciences of the United States of America. ,vol. 102, pp. 2602- 2607 ,(2005) , 10.1073/PNAS.0409402102
JEAN-PAUL VONSATTEL, RICHARD H. MYERS, THOMAS J. STEVENS, ROBERT J. FERRANTE, EDWARD D. BIRD, EDWARD P. RICHARDSON, Neuropathological classification of Huntington's disease. Journal of Neuropathology and Experimental Neurology. ,vol. 44, pp. 559- 577 ,(1985) , 10.1097/00005072-198511000-00003
Jens C Brüning, Jonathon Winnay, Susan Bonner-Weir, Simeon I Taylor, Domenico Accili, C.Ronald Kahn, Development of a Novel Polygenic Model of NIDDM in Mice Heterozygous for IR and IRS-1 Null Alleles Cell. ,vol. 88, pp. 561- 572 ,(1997) , 10.1016/S0092-8674(00)81896-6
A. L. Lumsden, T. L. Henshall, S. Dayan, M. T. Lardelli, R. I. Richards, Huntingtin-deficient zebrafish exhibit defects in iron utilization and development Human Molecular Genetics. ,vol. 16, pp. 1905- 1920 ,(2007) , 10.1093/HMG/DDM138
Jacqueline Shehadeh, Herman B. Fernandes, Melinda M. Zeron Mullins, Rona K. Graham, Blair R. Leavitt, Michael R. Hayden, Lynn A. Raymond, Striatal neuronal apoptosis is preferentially enhanced by NMDA receptor activation in YAC transgenic mouse model of Huntington disease. Neurobiology of Disease. ,vol. 21, pp. 392- 403 ,(2006) , 10.1016/J.NBD.2005.08.001
Jennifer R. Gatchel, Huda Y. Zoghbi, Diseases of unstable repeat expansion: mechanisms and common principles. Nature Reviews Genetics. ,vol. 6, pp. 743- 755 ,(2005) , 10.1038/NRG1691
Katarzyna Sieradzan, David M.A Mann, Alan Dodge, Clinical presentation and patterns of regional cerebral atrophy related to the length of trinucleotide repeat expansion in patients with adult onset Huntington's disease Neuroscience Letters. ,vol. 225, pp. 45- 48 ,(1997) , 10.1016/S0304-3940(97)00182-1