Feocromocitoma asociado a neurofibromatosis de von Recklinghausen

摘要: Pheochromocytoma associated with von Recklinghausen neurofibromatosis. A pheochromo cytoma is an adrenal gland tumor that secretes epinephrine and norepinephrine hormones, responsible for regulating heart rate blood pressure, among other functions. The condition can occur alone or in combination disorders, genetic environmental factors play a key role. Neurofibromato- sis-1 (NF-1) inherited "autosomal dominant" disorder one of the most common charac- terized by formation neurofibromas (tumors involving nerve tissue) skin, subcutaneous tissue, cranial spinal root nerves. NF1 generally diagnosed physical examination. There no cure NF1, but there are ways to treat some its effects. Neurofibromatosis arterial hypertension caused pheochromocytoma extremely rare, less frecuent than 1% childrens 10 years old, young adults. We present case infrequent association between neurofibromatosis woman newly hypertension. discuss underlying pathophysiological mechanisms clinical implications.