Hypertrophic Cardiomyopathy in Infants and Children

摘要: The definition and classification of the cardiomyopathies has been traditionally a complex quite variable subject. In 2006, American Heart Association issued scientific statement elaborated by task force experts that contemplated important development molecular genetics in recent years, to explain etiology diseases cardiac muscle, or cardiomyopathies, previously considered idiopathic (B.J. Maron et al., 2006a). document stated “Cardiomyopathies are an heterogeneous group myocardial associated with mechanical and/or electrical dysfunction usually, but not always, exhibit inappropriate ventricular hypertrophy dilation, originated variety causes, frequently genetic. Cardiomyopathies involve just heart part systemic disorders often lead cardiovascular death failure related disability”. Myocardial damage secondary coronary atherosclerosis, valve disease, congenital hypertension, is excluded from this definition. Primary metastatic tumors primarily affecting endocardium minimal absent neither included. also discourages use classical terminologies hypertrophic, dilated, restrictive because they have overlapping features mutate one type another during course disease. then classified into 2 groups, primary when there only involvement, if affected multiorganic involvement. (Table 1) divided genetic, acquired, mixed (genetic acquired).