摘要: There is increasing evidence that a cardiomyopathy with preferential, mild to moderate (at least in the early phase) RV involvement, characterized by some peculiar segmental wall motion abnormalities and adipose or fibro-adipose tissue infiltration, underlying anomaly wide spectrum of clinical conditions. At one end this stand malignant ventricular tachyarrhythmias which are infrequent generally symptomatic[8–12]. Common features majority cases frequent sometimes complex PVBs, mostly, though not exclusively, originating RV[3,11,13], may be asymptomatic, exercise-related only cases, often associated T-wave abnormalities. Then, at other we find patients without arrhythmias complaining precordial pain[7]. Physical examination minor form subgroups negative as, most non-invasive investigations. Diagnosis these thus mainly based on right ventriculography biopsy, although diagnostic criteria yet completely defined. So, now faced dilemma whether submit invasive investigations which, moment, seem appropriate approach.