Spliceosome integrity is defective in the motor neuron diseases ALS and SMA
作者： Hitomi Tsuiji , Yohei Iguchi , Asako Furuya , Ayane Kataoka , Hiroyuki Hatsuta
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摘要: … linking for the first time the selective vulnerability of motor neurons to spliceosome breakdown in Gems of ALS and SMA. Furthermore, targeting spliceosome and/or Gem stability in …
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