West syndrome: etiological and prognostic aspects.

作者: Kazuyoshi Watanabe

DOI: 10.1016/S0387-7604(97)00085-5

关键词:

摘要: West syndrome is a multi-etiological condition. Recent progress in perinatal medicine and the recent development of new neuroimaging techniques may have changed etiological panorama syndrome. Our study has disclosed an increasing percentage group decreasing doubtful group. The increase due to increased proportion very low-birthweight infants periventricular leucomalacia (PVL). Among various factors added long list causes syndrome, focal cortical dysplasia another newly emerging factor associated with this Patients unilateral more commonly partial seizures, but show infantile spasms transiently during infancy. They seizures preceding, combination or following spasms. Follow-up MRI necessary detect delayed myelination because it not at common ages onset PET useful further differentiate cryptogenic Although regarded as one intractable epilepsies, prognosis differs widely according etiology. also predict seizure psychomotor prognosis.

参考文章(78)
P. Dautreme, E. Mallet, B. Le Luyer, J. Boulloche, P. Tron, A prognostic study of cryptogenic infantile spasms Annales De Pediatrie. ,vol. 38, pp. 71- 74 ,(1991)
O. Dulac, Infantile spasms associated with cortical dysplasia and tuberous sclerosis Dysplasias of cerebral cortex and epilepsy. pp. 217- 225 ,(1996)
Hugh Jolly, Clinics in Developmental Medicine Journal of the Royal Society of Medicine. ,vol. 58, pp. 745- 745 ,(1965)
Peter Machin Jeavons, Brian Douglas Bower, Infantile spasms : a review of the literature and a study of 112 cases Spastic Society Medical Education and Information Unit in association with Heinemann Medical. ,(1964)
Solomon L. Moshé, Shlomo Shinnar, Luis A. Alvarez, Infantile spasms due to unilateral cerebral infarcts Pediatrics. ,vol. 79, pp. 1024- 1026 ,(1987)
C W Shepherd, O W Houser, M R Gomez, MR findings in tuberous sclerosis complex and correlation with seizure development and mental impairment. American Journal of Neuroradiology. ,vol. 16, pp. 149- 155 ,(1995)
H V Vinters, P J Rintahaka, J W Kevill, J G Curran, R Sankar, D A Shewmon, Microscopic cortical dysplasia in infantile spasms: evolution of white matter abnormalities. American Journal of Neuroradiology. ,vol. 16, pp. 1265- 1272 ,(1995)
Harry T. Chugani, W. Donald Shields, D. Alan Shewmon, Donald M. Olson, Michael E. Phelps, Warwick J. Peacock, Infantile spasms. I, PET identifies focal cortical dysgenesis in cryptogenic cases for surgical treatment Annals of Neurology. ,vol. 27, pp. 406- 413 ,(1990) , 10.1002/ANA.410270408
Eren Özek, M. Memet Özek, Mine Çalişkan, Aydin Sav, Selçuk Apak, Canan Erzen, Multiple pineal cysts associated with an ependymal cyst presenting with infantile spasm Childs Nervous System. ,vol. 11, pp. 246- 249 ,(1995) , 10.1007/BF00277661
B. Koo, P. A. Hwang, W. J. Logan, Infantile spasms: Outcome and prognostic factors of cryptogenic and symptomatic groups Neurology. ,vol. 43, pp. 2322- 2322 ,(1993) , 10.1212/WNL.43.11.2322