Laparoscopic-assisted surgical reconstruction of a rare congenital abdominal wall defect in two children misdiagnosed with prune-belly syndrome

摘要: Abstract Purpose Abdominal wall laxity is typically associated with prune-belly syndrome (PBS). Incomplete forms of PBS have been rarely reported only the abdominal laxity. Herein, we describe a rare congenital defect that has confused and illustrate laparoscopic-assisted surgical technique used for reconstruction. Materials methods Two boys symmetrical, bilateral absence or hypoplasia internal external oblique muscles no genitourinary abnormalities underwent reconstruction utilizing previously described by Firlit. Each patient had Ct scan which confirmed muscles. In one EMG data electrical activity obliques. Radiologic evaluation urinary tracts revealed abnormalities. The was plicated subcostal incisions. Results Both patients excellent cosmetic functional results weakness bulging lateral improvement symptoms. Conclusions We believe these two cases their defects are often misdiagnosed muscular deficiency separate from PBS. novel illustrated feasible highly successful possible other similar defects.