Hypoplastic left heart syndrome: current treatment options and outcome

摘要: Hypoplastic left heart syndrome (HLHS) represents a spectrum of lesions having in common hypoplasia the ventricle, association with aortic valve atresia or stenosis, mitral stenosis and arch. l The precise aetiology this lesion is unknown. Maintenance systemic circulation depends upon pulmonary venous blood reaching right atrium through an interatrial communication, which often restrictive. Common mixing oxygenated deoxygenated within ventricle occurs, then distributed both to lungs (via arteries) arterial duct. Coarctation aorta adjacent ductal insertion common, due extension tissue into aorta. As does not contribute cardiac output, perfusion coronary arteries myocardium dependent retrograde flow ascending via