Complex I deficiency due to selective loss of Ndufs4 in the mouse heart results in severe hypertrophic cardiomyopathy.
作者： Edward T. Chouchani , Carmen Methner , Guido Buonincontri , Chou-Hui Hu , Angela Logan
DOI: 10.1371/JOURNAL.PONE.0094157
关键词:
摘要: Mitochondrial complex I, the primary entry point for electrons into the mitochondrial respiratory chain, is both critical for aerobic respiration and a major source of reactive oxygen species…
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