Congenital absence of nasal bones.

摘要: Isolated congenital nasal malformation is rare; the isolated absence of any specific structure even rarer. They are related to craniofacial stenosis syndromes and facial cleft, which described in Tessier classification; also they can appear 58 complex genetic syndromes. Nasal malformations may be acquired as a consequence traumas, tumors, infectious diseases, or sequelae aesthetic surgery. Gorham's syndrome rare disease that produces spontaneous asymptomatic disappearance bone skeleton. In world literature, there no case with bones. This report 20-year-old patient who sought correction an defect produced by cartilaginous hump without presence The both bones failure development centers ossification. Through study embryological structure, explained.