Cholestasis Reveals Severe Cortisol Deficiency in Neonatal Pituitary Stalk Interruption Syndrome

作者: Francois-Xavier Mauvais , Emmanuel Gonzales , Anne Davit-Spraul , Emmanuel Jacquemin , Raja Brauner

DOI: 10.1371/JOURNAL.PONE.0147750

关键词:

摘要: Objectives Cholestasis has been reported during the course of congenital hypothalamic-pituitary deficiency, but crucial information is lacking regarding both its origin and prognosis. We aimed to characterize cholestasis factors contributing it in patients with deficiency due pituitary stalk interruption syndrome (PSIS).

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