Dermatofibrosarcoma protuberans. A clinico-pathological study of nineteen cases and review of world literature.

摘要: The clinical course, pathological features and response to treatment in a consecutive 16-years series of 19 cases dermatofibrosarcoma protuberans were studied. A review the world literature, comparing results ours too was performed. tumour, occurring at every age equally among females males, most commonly involves trunk without any particular pattern. disease usually runs an indolent course is often regarded lightly by patients as well physicians leading delayed conservative treatment. tumour has definite invasive metastatic potential considered low grade soft tissue sarcoma. To avoid mutilating surgery (and maybe metastases) later initial must be wide surgical excision including surrounding margin least 1 inch normal tissue. removal underlying deep fascia essential adequate resection will require skin graft replacement nearly instance. Follow up periods should no less than 3 years oncological service continued general practitioners because tumours may recur after considerable time, even apparently adequately treated patients.