Pediatric idiopathic dilated cardiomyopathy: A single center experience

摘要: Context: Idiopathic dilated cardiomyopathy (IDCM) is a severe illness with high mortality in the pediatric population. AIMS: To highlight our experience about clinical course and outcome of IDCM. Settings Design: Patients' files were reviewed retrospectively for diagnosed cases IDCM cardiology unit King Abdul Aziz University Hospital, Jeddah, Saudi Arabia, from Jan 2003 to Jun 2011. Materials Methods: Data full history, examination investigations recorded grouped according as alive well (group 1), symptomatic 2) worsened or dead 3). Statistical Analysis: was subjected descriptive analysis. Chi-square Student's paired t -test techniques used where appropriate. Spearman rank correlation survival analysis done. Results: Eighty three patients included presenting age median (range), i.e.,14 (2 months-12 years) females predominance 53 (63.9%). On presentation; cardiomegaly noted 72 (86.7%) increased lung vascularity 45 (54%). Sixty-one (74%) had ST segment T-wave changes on electrocardiogram, while same number left ventricular hypertrophy, 15 (18%) arrhythmias. Echocardiography records presentation at last follow-up showed significant difference several areas. Group 1 40 (48.2%), 2 23 (27.7%) 20 (24.1%) 3 including nine who died. Survival rate over years 78%. Older age, worse (Spearman's rho = 0.3, P 0.04). Conclusion: Majority subjects presented during first year life; Favorable correlated younger presentation.