An atypical presentation for primary sclerosing cholangitis.

摘要: We describe the clinical course of a group patients with primary sclerosing cholangitis who at presentation were diagnosed to have autoimmune hepatitis. The history one such patient is described in detail. also compare this atypical (group I) typical II) and hepatitis III) without IV) cholestasis. At presentation, mean AST groups I III was similar significantly higher than II (P < 0.05). Mean ALP but not so. Triaditis present all I, III, IV. Piecemeal necrosis multilobular collapse/fibrosis equally frequent Only response corticosteroids helped differentiate among groups. Groups IV responded by normalizing AST. In improved, never became normal. As disproportionately abnormal (ALP-predominant pattern), cholangiography performed, diagnosis made patients. recommend that be performed early suspected partially respond develop an ALP-predominant pattern.