Uses of inorganic pyrophosphates
作者： Michael J. Welsh
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摘要: Pharmaceutical compositions comprising an inorganic pyrophosphate (PPi) in a form that renders the PPi accessible to ABC proteins when administered subject vivo, as well use of for treating subjects having disease or disorder associated with inappropriate inadequate protein activity (e.g., cystic fibrosis, multi drug resistance, Zellweger's Syndrome) is disclosed.
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