Peripartum anesthetic management of a parturient with inherited factor v deficiency.

作者: Sonia Vaida , Hamid Al-Mondhiry , Dmitri Bezinover , Lauren Welsh , Serdar Ural

DOI: 10.1097/ACC.0B013E31829EC0B7

关键词:

摘要: Inherited Factor V deficiency is a rare bleeding disorder. We describe the genetic analysis and anesthetic management of parturient with severe who presented in spontaneous labor. Good hemostatic conditions were obtained prophylactic fresh frozen plasma administration 10 mL/kg. Detailed by next-generation sequencing identified several relevant mutations coding part (F5) gene our patient, her parents, newborn.

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