Common Variable Immunodeficiency
作者： Maria Pia Bondioni , Annarosa Soresina , Vassilios Lougaris , Diego Gatta , Alessandro Plebani
DOI: 10.1097/RCT.0B013E3181CAD9DA
关键词:
摘要: Background: Common variable immunodeficiency (CVID) is the most common symptomatic primary characterized by recurrent respiratory tract infections, mainly sustained encapsulated bacteria, that may cause irreversible changes in lungs. Methods: Forty patients with CVID were evaluated computed tomography of lung; 20 these underwent tomographic follow-up a 5-year period, during which immunoglobulin replacement therapy was regularly performed. Results: Pulmonary present 65% patients; bronchiectases 65.38%. The incidence pulmonary nodules very high (38.46%) and correlated splenomegaly (70%) autoimmune phenomena (80%). Conclusions: Our study underscores essential role imaging, particular tomography, identification monitoring lesions large cohort patients, contributing at same time to select more risk develop nodular potentially use appropriate therapeutic strategies.
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