Sources of propionate in inborn errors of propionate metabolism.
作者： G.N. Thompson , J.H. Walter , J.-L. Bresson , G.C. Ford , S.L. Lyonnet
DOI: 10.1016/0026-0495(90)90084-P
关键词:
摘要: … Unlike metabolic conditions such as maple syrup urine disease, in which careful dietary … generally results in good metabolic control, the response of disorders of propionate metabolism …
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