Vasculitis of the central nervous system.

摘要: Abstract Angiitis of the CNS remains a poorly understood form vascular inflammatory disease. Primary angiitis or PACNS, disease once considered extremely rare, recently has been reported more frequently. Traditional views PACNS held it to be relentless and uniformly fatal if untreated, but is now viewed as heterogeneous, with some relatively benign subsets. Its pathophysiology understood. Secondary vasculitis can occur variety other conditions diseases; each requires different diagnostic therapeutic approach. Regardless whether primary secondary considered, an understanding limitations currently available neurodiagnostic investigations essential.