Three complementation groups in Cockayne syndrome.
作者： A.R. Lehmann
DOI: 10.1016/0027-5107(82)90115-4
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摘要: Abstract After 16 Jm −2 of UV-irradiation non-dividing normal cells recover rates RNA synthesis within 24h, whereas in from donors with Cockayne syndrome (CS) the rate gradually declines. Cultures a mixed population 2 CS were fused polyethylene glycol; subsequently they UV-irradiated and was measured autoradiographically mono-, bi-, multinuclear cells. Genetic complementation indicated by high levels bi- when compared mononuclear Using this assay, 11 strains have been assigned to three groups: into group A, 8 B 1 C. The strain C is derived an individual who also had xeroderma pigmentosum (XP), sole known representative XP-complementation B.
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