摘要: Early diagnosis permits preventive therapy to preempt development of organ damage. In all diagnosed patients, both symptomatic and asymptomatic, pharmacologic is lifelong, maintenance treatment prevent copper toxicity mandatory. Patients with either fulminant hepatic failure or insufficiency unresponsive medical should be considered for orthotopic liver transplantation, which effectively cures Wilson's disease. Prognosis excellent compliant patients receiving therapy.
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