The “adult” form of the scimitar syndrome

摘要: One hundred twenty-two cases of the adult form scimitar syndrome were collected from different cardiologic centers. The clinical, radiographic and hemodynamic findings are described. is defined as an anomalous right pulmonary venous drainage, partial or complete, to inferior vena cava. Additional characteristics this such hypoplasia abnormalities vascular supply lung, dextrocardia bronchial segmentation common; bronchiectases rare. left shunt was less than 50% in 100 122 patients. arterial pressures normal 94 patients slightly elevated 28. A follow-up study these showed that, without surgical correction, they lead a life. An awareness may avoid unnecessary invasive diagnostic procedures treatment for most