Consideraciones anestésicas en las inmunodeficiencias primarias

摘要: Primary immunodeficiencies are a group of mostly hereditary, or congenital, disorders. Some cases, however, show no hereditary pattern despite an evident familial distribution. The incidence these cases is variable and the most frequent them immunoglobulin A deficiency. Many pediatric disorders that occasionally so serious patient does not survive first year life due to development systemic infections. In other survival much longer it possible find adult carriers in routine clinical practice. These less aggressive form part specific syndromes must be recognized appropriate anesthetic management can planned. We review characteristics primary may relevant patients.