Duration of prion disease is longer in Japan than in other countries.
作者： Kiwamu Nagoshi , Atsuko Sadakane , Yosikazu Nakamura , Masahito Yamada , Hidehiro Mizusawa
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摘要: Background: Prion diseases are untreatable, progressive, and fatal brain disorders that occur worldwide, the annual incidence rate is approximately 1 case per million people. The duration of these in Japan unclear.Methods: Based on data from April 1999 through 4 September 2008 provided by Japanese Creutzfeldt-Jakob disease (CJD) surveillance program, we analyzed its relationship with clinical features. Duration was assumed to be time onset death.Results: Evaluation committee indicated during observed period 1128 individuals received a diagnosis prion were registered program. Mean 855 patients who died 17.4 months. Overall, 46.0% within year 77.2% less than 2 years. Among those sporadic disease, which represented 77.0% cases, mean 15.7 months, while surveyed European Creutzfeldt Jakob Disease Surveillance Network (EUROCJD) only 5 months.Conclusions: among much longer Western countries conducting diseases. This finding suggests characteristics system for providing life-sustaining treatment fatal, progressive related illnesses.
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