Arrhythmogenic Right Ventricular Cardiomyopathy: Clinical Assessment and Differential Diagnosis

摘要: Arrhythmogenic right ventricular cardiomyopathy (ARVC) is an inherited cardiovascular disorder leading to life-threatening arrhythmias, progressive biventricular dysfunction, and heart failure. Sudden death can be the unique feature of disease. Genetic studies indicate that ARVC should considered a disease desmosome dysfunction. Diagnosis remains clinical challenge mainly in its early stages patients with minimal imaging structural abnormalities. shares some common features other cardiac diseases, such as RV outflow tract tachycardia, Brugada syndrome, dilated cardiomyopathy, myocarditis, due arrhythmic expressivity involvement. based on major minor criteria listed Revised Task Force Criteria.