Pathologic evidence of extensive left ventricular involvement in arrhythmogenic right ventricular cardiomyopathy.

摘要: Abstract Arrhythmogenic right ventricular cardiomyopathy (also known as arrhythmogenic dysplasia) is characterized by adipose or fibroadipose tissue replacement of the myocardium, whereas left ventricle substantively spared. Two cases disease with evidence extensive involvement at pathologic examination are described. Hearts from two patients who died suddenly showed full-thickness fatty infiltration associated (> 50% myocardial thickness). These findings might explain reported clinical features dysfunction in a subset cardiomyopathy. In view biventricular disease, it should simply be termed “arrhythmogenic cardiomyopathy.”