Imaging of congenital lipoid adrenal hyperplasia.
作者： Ehiichi Kohda , Hiroya Yamazaki , Hiromi Hisazumi , Yoshiyuki Tutumi , Tsutomu Ogata
DOI: 10.1007/S11604-005-1553-X
关键词:
摘要: This article describes the specific radiological findings of congenital lipoid adrenal hyperplasia (lipoid CAH) in a phenotypic female and karyotypic 46XY infant. Radiological examination showed enlarged bilateral glands with fatty accumulation spared medulla. These are key to differentiating CAH from diseases that cause insufficiency during early infancy, including other forms hyperplasia.
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