Sodium 4-phenylbutyrate downregulates Hsc70: implications for intracellular trafficking of ΔF508-CFTR
作者： Ronald C. Rubenstein , Pamela L. Zeitlin
DOI: 10.1152/AJPCELL.2000.278.2.C259
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摘要: The most common mutation of the cystic fibrosis transmembrane conductance regulator (CFTR), ΔF508, is a trafficking mutant that has prolonged associations with molecular chaperones and rapidly d...
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