Progressive Systemic Sclerosis Sine Scleroderma

摘要: Four patients, a man aged 51 and 3 women 59, 69, 71, died of progressive systemic sclerosis yet had minimal or no evidence cutaneous disease (scleroderma). In addition to illustrating the great variability in clinical course sclerosis, these cases serve point up difficulties involved recognition this condition prior development typical skin changes. When patients are encountered with such problems as unexplained esophageal intestinal hypomotility malabsorption, both, myocardial disease, pulmonary fibrosis, diagnosis should be suspected from certain characteristic roentgenographic findings, may confirmed, at least those by histologic examination tissue obtained operation.